pseudohypoaldosteronism: a case report
نویسندگان
چکیده
a four day old female infant was admitted because of poor feeding, vomiting and jaundice. laboratory examination showed hyperkalemia, mild hyponatremia and renal tubular acidosis type 4. serum aldosterone and plasma renin activity were elevated but serum cortisol, 17 -hydroxyprogesterone, acth, 24 hour urinary 17- ketoste roid, pregnanetriol, renal function and sonogram were normal and hence pseudohypoaldosteronism type i (pha 1) was differentiated from congenital adrenal hyperplasia (cah) and other metabolic disorders. these abnormalities were corrected with sodium chloride supplementation.
منابع مشابه
PSEUDOHYPOALDOSTERONISM: A CASE REPORT
A four day old female infant was admitted because of poor feeding, vomiting and jaundice. Laboratory examination showed hyperkalemia, mild hyponatremia and renal tubular acidosis type 4. Serum aldosterone and plasma renin activity were elevated but serum cortisol, 17 -hydroxyprogesterone, ACTH, 24 hour urinary 17- ketoste roid, pregnanetriol, renal function and sonogram were normal and henc...
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عنوان ژورنال:
medical journal of islamic republic of iranجلد ۸، شماره ۱، صفحات ۵۳-۵۵
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